Archives of Head and Neck Surgery
https://www.archivesheadnecksurgery.com/article/doi/10.4322/ahns.2020.0002
Archives of Head and Neck Surgery
Case Report Miscellaneous

Extramedullary hematopoiesis of the middle ear

Vanessa Ribeiro Orlando, Marcelo Castro Alves de Sousa, Nicodemos José Alves de Sousa

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Abstract

Extramedullary hematopoiesis is characterized by the production of blood at sites outside the bone marrow that occurs due to an increased demand of the hematopoietic system as a consequence of chronic anemia associated with ineffective bone marrow response. Theoretically, any organ may be involved in extramedullary hematopoiesis. In this case report, a patient with sickle cell anemia developed an extremely rare presentation of extramedullary hematopoiesis in the middle ear. Therefore, extramedullary hematopoiesis should be included as a differential diagnosis of middle ear masses in patients with chronic anemia.

Keywords

anemia, sickle cell; ear, middle; hematopoiesis; hematopoiesis, extramedullary; hemoglobin sickle cell disease.

References

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